Primary Cutaneous Rosai-Dorfman Disease of the Scalp

Cutaneous Rosai-Dorfman disease.

Rosai-Dorfman disease (RDD) is a rare benign proliferative disorder of histiocytes in the lymph nodes with or without extranodal involvement. RDD limited to the skin without nodal involvement, known as cutaneous Rosai-Dorfman disease, is very rare. We describe a 34-year-old female with RDD of the skin over the chest. A large nodule with satellite lesions was excised for histopathological examin...

Rosai-Dorfman disease with primary cutaneous manifestations--a case report.

Rosai-Dorfman disease (sinus histiocytosis with massive lymphadenopathy) is a benign systemic proliferative disorder of histiocytes resembling the sinus histiocytes of lymph nodes. The typical clinical features of this disease include bilateral painless lymphadenopathy, fever, and polyclonal hyperglobulinaemia. The condition may present with extranodal involvement in 43% of cases, and cutaneous...

Cutaneous Rosai- Dorfman Disease with Associated Uveitis

56 PRACTICAL DERMATOLOGY AUGUST 2014 R osai-Dorfman disease (RDD), or sinus histiocytosis with massive lymphadenopathy (SHML) is a benign lympho-histiocytic proliferative disorder initially described with bilateral painless lymphadenopathy (90 percent), fever, leukocytosis, elevated ESR, anemia, and polyclonal hypergammaglobulinemia (90 percent).1 RDD presents with cervical adenopathy most comm...

Cutaneous Rosai-Dorfman disease: a case report.

A 40-year-old female presented with a 2-year history of asymptomatic nodules on her lower extremity. Symptoms began with a small dark spot on the right thigh, which progressively enlarged. She then developed similar nodules on her right leg and a lesion on her left buttock. On physical exam, her right proximal lateral thigh revealed a 10 cm x 6 cm indurated, pink-brown, heterogeneous plaque wit...

Atypical presentation and dermoscopic evaluation of cutaneous Rosai-Dorfman Disease.